RESUMO
An 8-year-old boy with recurrent acute bleeding of lymphangioma of the left orbit is described. D-dimer levels increased as the size of the mass became stable, showing the effect of fibrinolysis within the hemorrhagic mass after clotting. D-dimer levels confirmed the possible use of conservative management of this lymphangioma.
Assuntos
Hemorragia Ocular/sangue , Produtos de Degradação da Fibrina e do Fibrinogênio/metabolismo , Linfangioma/sangue , Neoplasias Orbitárias/sangue , Biomarcadores Tumorais/sangue , Criança , Diagnóstico Diferencial , Hemorragia Ocular/diagnóstico , Hemorragia Ocular/etiologia , Seguimentos , Humanos , Linfangioma/complicações , Linfangioma/diagnóstico , Imageamento por Ressonância Magnética , Masculino , Neoplasias Orbitárias/complicações , Neoplasias Orbitárias/diagnóstico , Tomografia Computadorizada por Raios XRESUMO
An 8.5-year-old girl who presented with chronic cough and hemoptysis underwent a CT scan of the chest showing diffuse mediastinal and parenchymal infiltration and pleural effusion, and laboratory findings showed disseminated intravascular coagulation. Disseminated lymphangiomatosis was diagnosed after an open-lung biopsy. She was treated by systemic steroids, interferon, tamoxifen, chemotherapy, and radiation but died of respiratory failure and disseminated intravascular coagulation 2 years after the diagnosis. This patient represents a rare presentation of diffuse pulmonary lymphangiomatosis together with disseminated intravascular coagulation, involving both the mediastinum and pulmonary parenchyma, in a child.
Assuntos
Coagulação Intravascular Disseminada/etiologia , Linfangioma/complicações , Neoplasias Torácicas/complicações , Corticosteroides/uso terapêutico , Protocolos de Quimioterapia Combinada Antineoplásica/administração & dosagem , Protocolos de Quimioterapia Combinada Antineoplásica/uso terapêutico , Criança , Terapia Combinada , Ciclofosfamida/administração & dosagem , Dactinomicina/administração & dosagem , Dispneia/tratamento farmacológico , Dispneia/etiologia , Evolução Fatal , Feminino , Humanos , Linfangioma/sangue , Linfangioma/tratamento farmacológico , Linfangioma/radioterapia , Mediastino/patologia , Cuidados Paliativos , Radioterapia Adjuvante , Tamoxifeno/administração & dosagem , Neoplasias Torácicas/sangue , Neoplasias Torácicas/tratamento farmacológico , Neoplasias Torácicas/radioterapia , Trombocitopenia/etiologia , Vincristina/administração & dosagemRESUMO
A case of mesenteric cystic lymphangioma revealed by hypochromic anemia and abdominal pain, secondary to an intracystic hemorrhage is reported in a 4-year old child. Etiology, pathology, diagnosis, treatment and prognosis of mesenteric lymphangioma in children are reviewed.